Cystic Fibrosis Nursing | Cystic Fibrosis Symptoms, Causes, Treatment, NCLEX Review

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Cystic fibrosis NCLEX nursing review: Cystic fibrosis is a genetic disorder that causes the exocrine glands to work incorrectly.

This can lead to major complications that affect the respiratory, digestive (pancreas, liver, intestines), integumentary, and reproductive systems along with the sinuses.

What are exocrine glands? These are glands that produce and transfer it’s secretions (ex: mucous, tears, sweat, digestive enzymes) via DUCTS to it’s intended area of the body rather than directly into the bloodstream like the endocrine glands.

In cystic fibrosis, there is a gene that is mutated that prevents the exocrine gland from working properly. It is called the CFTR gene!

The CFTR gene, which stands for cystic fibrosis transmembrane regulator, is a protein that controls the channels of sodium and chloride. Hence the sodium and water transport in and out of the cell, and these channels are within the membrane of the cells that makes our sweat, mucous, tears, and digestive enzymes.

However, in CF these channels don’t work properly. Therefore, normally these channels would properly regulated sodium and water transport in and out of the cells, which helps control the flow of water within these structures among other things. But this is not what happens in a person with cystic fibrosis.

The mucous is thick and sticky rather than thin and slippery. This mucous will block the airways in the lower respiratory system and block the pancreatic duct from delivering pancreatic enzymes. In addition, the sweat glands produce excessive amounts of salt.

CF tends to affect Caucasians and males more. The current median life expectancy of a person with cystic fibrosis is 37 years of age (source: NIH.gov). It is currently diagnosed with a sweat test where pilocaprine and electric current is delivered to the skin to make it sweat. The amount of salt in the sweat is measured. Results 60 mmol/L or more is considered positive for CF.

Nursing interventions to cystic fibrosis include: chest physiotherapy (chest PT), monitor for complications, educating about PEP devices, preventing infection, administering medications and more (see the video for a detailed review of the nursing interventions)

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Hello Everyone!! Thank you so much for watching this video. Don't forget about:
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RegisteredNurseRN
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I have cystic fibrosis and I’m a Labor and delivery nurse! I am so blessed to be healthy ❤️ you did a fabulous job with this video!! Hopefully many others can learn from your video and understand this disease a little better.

kaittoense
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To be honest, she is far more knowledgeable than some doctors

wosuibian
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I just want to say thank you so much for all you do! I used your videos throughout nursing school, and I also used them to prepare for the Nclex-RN. I passed with 75 questions. I could't have done it without God and your amazing videos!

maryamaboko
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Hi :) I passed my NCLEX-RN last December 2017 with the help of all your videos.👍🏼 Although i'm already a passer, every once in a while I still check your videos to refresh my mind, and watching you again reminds me of my review days. :) I am recommending your channel to all my friends here in the Philippines who are going to take the exam too.. continue helping foreign nurses with your videos! God bless you sarah...❤️

janinay
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And i finally understand cystic fibrosis.. at this point i literally like a video even before it plays ..as long as its by you.i know its going to be great..thank you sooo much

nyamurungibtumusiime
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Finally a channel that actually teaches, gets straight to the point and doesn't beg for likes and subscription
thank you so much, liked and subscribed

yousifmq
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Recently took the NGN-NCLEX Version. Passed the NCLEX-RN on the second try. Your videos are definitely helpful. Highly Recommended. Thank you.

johnnypatch
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Hi Sarah, I just want to say thank you!😘 I took my nclex last week of march and passed! I’m blessed and grateful because i watched some of your videos 3 weeks before my exam😊 God bless you always!❤️🙏🏻❤️

wiseeggroll
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Best YouTube channel for nursing. Hands down! 🙏🏼

Skytall
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I would like to take this opportunity and thank you for the good work you are doing . I took my Nclex last week on 27th and passed .I watched all your videos and all i can say is you are heaven sent. May God bless you abundantly. Am forever grateful.

hannahmwangi
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As a cfer your research was really good!!! I hate when I hear people talk about about cf that’s not accurate

purposewithmalika
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im gonna start advertising your channel to all the nursing students I know. you gotta get the credit that you deserve. all your videos are very helpful. thank you!

nuelmow
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You've honestly helped me pass every test I've had so far. We have so much to learn and our professors don't have time to teach us everything so we are leg to learn it for ourselves. I dont learn well by just reading my books, so I correlate your information with what our books say and it helps soo much! And I learned ABGs SPECIFICALLY from your videos (not my professors)and the tic tac toe method. Thank you so much!! I appreciate you so much.

kelseytam
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This is the greatest youtube channel I could've ever discovered!

bolt
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Hi nurse sarah i just want to say thank you so much for your lecture videos it really really helped me a lot in passing my nursing licensure exam here in phillipines 😊😇keep posting more nursing lecture videos.GOD BLESS YOUR FAMILY😊

vanessyruzzle
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Hi there Sarah! Your channel really is a blessing for me, a home care nurse adjusting in a hospital ward... If I may, it would be awesome if you could make a lecture on interpreting lab values/ecg reading... Hope you would consider.. Thanks!!

myth
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I love this Video! I have Cystic Fibrosis and I'm 27! Awesome! my PFT's are almost 100% however, I do have all of these issues even though my lungs are "healthy" are moving air. Bloody Sputum, Cultured Bacterias (staph, pseudo, achro, etc), Liver Issues, CFRDiabetes- Amazing how much information this video provides and it is organized beautifully.

schonlift
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Your the best. Please don't stop doing what you love BEST. I can only learn from your video. My professors are story tellers, no one does it best than SARAH REGISTER NURSE. 🔥🔥💕💕

chizobanweke
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I had a flutter valve after my open heart surgery. It was green so everyone called it a pickle! It helped immensely! Love your videos!

coopyjay