Fetal Hemivertebra with Diastematomyelia

Fetal Hemivertebra with Diastematomyelia
Hemivertebra
• Rare congenital spinal malformation; one side of the vertebral body develops; resulting in scoliosis, lordosis, or kyphosis.
• Incidence hemivertebra - 0.5–1.0 per 1000 births
• Results from abnormal distribution of the intersegmental arteries of the vertebral column.
• Isolated or involve multiple segments or associated with congenital anomalies of spine, ribs, and limbs.
• Syndromes; Jarcho-Levin syndrome, Klippel-Fiel syndrome, VATER, VACTERL syndrome
Diastematomyelia
• Rare form of spinal dysraphism; sagittal cleft in spinal cord, conus medullaris, and/or filum terminale with splaying of the posterior vertebral elements.
• Type I - two hemicords, contained within in two separate dural sheaths and separated by a rigid, osseocartilaginous median septum.
• Type II - two hemicords housed in a single dural sheath and separated by a nonrigid, fibrous median septum
Syringomyelia
• Any cavity within the substance of the spinal cord that may or may not communicate with the central canal.
• Dissection of the ependymal lining of the central canal and CSF collection within the cord itself. Therefore, the collection does not have an ependymal lining.
• Characteristically, located in cervicothoracic cord, with C2 to T9 being the most common location.
Fetal Medicine help save lives. For further quires please contact
Dr Ashutosh Foetal & Genetic Clinic; E 874, Chittaranjan Park, New Delhi 110019

[drashutoshgupta]

If any concerns, please reach out to:
• www.fetalandgeneticclinic.com
• 9953728760